Collagenofibrotic glomerulopathy in a kidney transplant recipient: A first report

dc.contributor.authorJdiaa, Sara S.
dc.contributor.authorMoeckel, Gilbert W.
dc.contributor.authorK̈foury, Hala Kassouf
dc.contributor.authorMedawar, Walid A.
dc.contributor.authorAbu-Alfa, Ali K.
dc.contributor.departmentInternal Medicine
dc.contributor.departmentPathology and Laboratory Medicine
dc.contributor.departmentDivision of Nephrology and Hypertension
dc.contributor.facultyFaculty of Medicine (FM)
dc.contributor.institutionAmerican University of Beirut
dc.date.accessioned2025-01-24T11:43:11Z
dc.date.available2025-01-24T11:43:11Z
dc.date.issued2021
dc.description.abstractCollagenofibrotic glomerulopathy (CG) is a rare disease characterized by the deposition of collagen type 3 fibrils in the glomeruli. Patients may have proteinuria, hematuria, and/or renal dysfunction. CG is considered a progressive disease with variable rates of progression. The definitive diagnosis is made by electron microscopy with the presence of characteristic subendothelial and mesangial curved, comma-like, banded collagen type 3 fibers of 40–65 nm periodicity. We are reporting the first case of CG in a kidney transplant recipient with kidney disease of unknown cause. © 2020 The American Society of Transplantation and the American Society of Transplant Surgeons
dc.identifier.doihttps://doi.org/10.1111/ajt.16399
dc.identifier.eid2-s2.0-85097957933
dc.identifier.pmid33206467
dc.identifier.urihttp://hdl.handle.net/10938/30227
dc.language.isoen
dc.publisherBlackwell Publishing Ltd
dc.relation.ispartofAmerican Journal of Transplantation
dc.sourceScopus
dc.subjectClinical research/practice
dc.subjectGenetics
dc.subjectKidney transplantation/nephrology
dc.subjectRecurrent disease
dc.subjectCollagen type iii
dc.subjectHumans
dc.subjectKidney diseases
dc.subjectKidney glomerulus
dc.subjectKidney transplantation
dc.subjectProteinuria
dc.subjectAzathioprine
dc.subjectCalcineurin inhibitor
dc.subjectCollagen type 3
dc.subjectCollagen type 4
dc.subjectCreatinine
dc.subjectCyclosporine
dc.subjectDipeptidyl carboxypeptidase inhibitor
dc.subjectMycophenolate mofetil
dc.subjectPrednisone
dc.subjectTacrolimus
dc.subjectAdult
dc.subjectAlbuminuria
dc.subjectArticle
dc.subjectCapillary basement membrane
dc.subjectCase report
dc.subjectClinical article
dc.subjectCollagen fiber
dc.subjectCollagen fibril
dc.subjectCollagenofibrotic glomerulopathy
dc.subjectCreatinine blood level
dc.subjectCytoplasm
dc.subjectDiabetes mellitus
dc.subjectDrug substitution
dc.subjectEndothelium cell
dc.subjectEpithelium cell
dc.subjectFibrosing alveolitis
dc.subjectFollow up
dc.subjectGlomerulopathy
dc.subjectGlomerulus capillary
dc.subjectGlucosuria
dc.subjectGraft recipient
dc.subjectHematuria
dc.subjectHuman
dc.subjectHyaline degeneration
dc.subjectHypertension
dc.subjectImmunohistochemistry
dc.subjectImmunosuppressive treatment
dc.subjectIraqi
dc.subjectKidney biopsy
dc.subjectKidney cortex
dc.subjectLeg edema
dc.subjectLymphocyte
dc.subjectMale
dc.subjectMesangium
dc.subjectMicroscopy
dc.subjectPlasma cell
dc.subjectPriority journal
dc.subjectSclerosis
dc.subjectAdverse event
dc.subjectGlomerulus
dc.subjectKidney disease
dc.titleCollagenofibrotic glomerulopathy in a kidney transplant recipient: A first report
dc.typeArticle

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