Perioperative Autonomic Dysfunction in a Patient with Charcot-Marie-Tooth Disease: A Case Report

dc.contributor.authorMaroun, Wissam
dc.contributor.authorAbi Shadid, Carol
dc.contributor.authorFayed, Mohamed
dc.contributor.authorFoz, Carine
dc.contributor.authorBeresian, Jean
dc.contributor.authorOseili, Ahmad
dc.contributor.departmentAnesthesiology
dc.contributor.facultyFaculty of Medicine (FM)
dc.contributor.institutionAmerican University of Beirut
dc.date.accessioned2025-01-24T11:40:33Z
dc.date.available2025-01-24T11:40:33Z
dc.date.issued2023
dc.description.abstractAutonomic dysfunction can lead to unexpected hemodynamic instability during surgery, and best practices for the perioperative care of patients with this condition are not well-defined. We report the case of a 63-year-old woman with Charcot-Marie-Tooth disease who experienced perioperative autonomic dysfunction characterized by severe fluctuations in blood pressure while under spinal anesthesia. However, <1 month later, a second hip surgery performed under general anesthesia with special precautions resulted in an uncomplicated perioperative course, with only mild fluctuations in blood pressure. © 2023 Wolters Kluwer Health. All rights reserved.
dc.identifier.doihttps://doi.org/10.1213/XAA.0000000000001722
dc.identifier.eid2-s2.0-85171240139
dc.identifier.pmid37703136
dc.identifier.urihttp://hdl.handle.net/10938/29516
dc.language.isoen
dc.publisherWolters Kluwer Health
dc.relation.ispartofA and A Practice
dc.sourceScopus
dc.subjectAnesthesia, general
dc.subjectAnesthesia, spinal
dc.subjectBlood pressure
dc.subjectCharcot-marie-tooth disease
dc.subjectFemale
dc.subjectHumans
dc.subjectMiddle aged
dc.subjectPerioperative care
dc.subjectAlprazolam
dc.subjectBudesonide
dc.subjectBupivacaine
dc.subjectCreatinine
dc.subjectEtomidate
dc.subjectFentanyl
dc.subjectFluoxetine
dc.subjectMidazolam
dc.subjectOxcarbazepine
dc.subjectPhenylephrine
dc.subjectPregabalin
dc.subjectRinger lactate solution
dc.subjectRocuronium
dc.subjectSalbutamol
dc.subjectSevoflurane
dc.subjectSugammadex
dc.subjectZolpidem
dc.subjectAdult
dc.subjectAnaphylaxis
dc.subjectAnesthesia level
dc.subjectArticle
dc.subjectAsthma
dc.subjectAutonomic dysfunction
dc.subjectAutonomic neuropathy
dc.subjectBlood pressure fluctuation
dc.subjectCapnometry
dc.subjectCase report
dc.subjectClinical article
dc.subjectCrystalloid
dc.subjectDermatome
dc.subjectElectrocardiogram
dc.subjectEnd tidal carbon dioxide tension
dc.subjectFemoral neck fracture
dc.subjectGeneral anesthesia
dc.subjectHeart arrest
dc.subjectHeart stress
dc.subjectHemoglobin blood level
dc.subjectHereditary motor sensory neuropathy
dc.subjectHip pain
dc.subjectHip surgery
dc.subjectHuman
dc.subjectHypertension
dc.subjectKnee surgery
dc.subjectLower limb
dc.subjectMajor depression
dc.subjectMean arterial pressure
dc.subjectNeuropathic pain
dc.subjectParalysis
dc.subjectParesthesia
dc.subjectPerioperative period
dc.subjectPeriprosthetic fracture
dc.subjectPhysiotherapy
dc.subjectRecovery room
dc.subjectResuscitation
dc.subjectSpinal anesthesia
dc.subjectThorax radiography
dc.subjectTotal hip replacement
dc.subjectUrea nitrogen blood level
dc.subjectComplication
dc.titlePerioperative Autonomic Dysfunction in a Patient with Charcot-Marie-Tooth Disease: A Case Report
dc.typeArticle

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