Aortopulmonary window in adults: A rare entity leading to Eisenmenger syndrome
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Blackwell Publishing Inc.
Abstract
An aortopulmonary window (APW) is a rare congenital heart defect involving an abnormal communication between the ascending aorta and the pulmonary trunk with separate aortic and pulmonary valves. This defect accounts for 0.2% of all congenital cardiac anomalies and if left untreated can lead to Eisenmenger syndrome, severe pulmonary hypertension, heart failure, and poor survival. The authors herein present a case of APW type III with Eisenmenger syndrome in an adult patient whose initial complaint was cyanosis, and provide a thorough review of the literature of cases of APW with Eisenmenger syndrome that have survived into adulthood. © 2019 Wiley Periodicals, Inc.
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Keywords
2d echocardiography, Cardiac imaging, Color doppler, Congenital heart defects, Congenital heart disease, Adult, Aortopulmonary septal defect, Echocardiography, Eisenmenger complex, Humans, Iron, Atrial situs solitus, Auscultation, Cardiovascular disease, Case report, Clinical article, Clinical feature, Color doppler flowmetry, Cyanosis, Digital clubbing, Dyspnea, Heart catheterization, Heart palpitation, Heart right ventricle hypertrophy, Human, Iron therapy, Jugular venous distention, Levocardia, Lung insufficiency, Male, Physical examination, Pigeon thorax, Priority journal, Review, Systolic heart murmur, Transthoracic echocardiography, Vein disease, Complication, Diagnostic imaging, Procedures