Successful treatment of severe aplastic anemia with syngeneic stem cell transplantation in the setting of active disseminated mucormycosis
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Elsevier B.V.
Abstract
Severe aplastic anemia (SAA) is a hematological disease resulting in pancytopenia due to bone marrow failure. Treatment consists of immunosppressive therapy, or allo-SCT. Patients with aplastic anemia are predisposed to invasive fungal infections due to mucormycosis. Till now, syngeneic SCT in the context of active mucormycosis infection for patients with severe aplastic anemia is lacking in the literature. Here, we report a case of severe aplastic anemia with disseminated mucormycosis infection undergoing syngeneic transplant. © 2019 The Authors
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Mucormycosis, Severe aplastic anemia, Syngeneic transplantation, Amphotericin b lipid complex, Cd34 antigen, Clarithromycin, Contrast medium, Cyanocobalamin, Cyclosporine, Eltrombopag, Erythropoietin, Fludarabine, Granulocyte colony stimulating factor receptor, Hemoglobin, Insulin, Linezolid, Piperacillin plus tazobactam, Posaconazole, Thymocyte antibody, Voriconazole, Abdominal radiography, Abscess drainage, Add on therapy, Adult, Antibiotic therapy, Antifungal therapy, Aplastic anemia, Article, Bacterial growth, Borrelia infection, Brain tomography, Bronchoalveolar lavage fluid, Candida tropicalis, Candidiasis, Case report, Chronic sinusitis, Clinical article, Combination drug therapy, Computer assisted tomography, Consciousness, Consciousness disorder, Debridement, Disease activity, Disease severity, Drug substitution, Drug withdrawal, Enterococcal infection, Enterococcus faecalis, Epistaxis, Erythrocyte transfusion, Fever, Fungus hyphae, Graft versus host reaction, Haemophilus parainfluenzae, Hematocrit, Hemoglobin blood level, Human, Image guided biopsy, Immunosuppressive treatment, Inguinal region, Insulin dependent diabetes mellitus, Insulin treatment, Iraq, Lethargy, Leukocyte count, Lung biopsy, Lung nodule, Magnetic resonance venography, Male, Medical history, Methicillin resistant staphylococcus aureus, Mycosis, Neuroimaging, Neutropenia, Pancytopenia, Paroxysmal nocturnal hemoglobinuria, Pelvis radiography, Platelet count, Priority journal, Recurrent disease, Right lung, Somnolence, Spleen abscess, Stem cell transplantation, Systemic mycosis, Thorax radiography, Thrombocyte transfusion, Transplantation conditioning, Vitamin blood level, Whole body radiation