Arrhythmogenic ventricular cardiomyopathy and sudden cardiac death: Left or right?

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Springer New York LLC

Abstract

Arrhythmogenic right ventricular cardiomyopathy is a leading cause of sudden cardiac death among athletes in Italy and the Mediterranean region. Although it often involves the right ventricle causing scarring, dilation, systolic impairment with aneurysm formation, it can also involve the left ventricle or present as isolated left ventricular cardiomyopathy. Cardiac magnetic resonance imaging is considered the gold standard in confirming the diagnosis. We summarize four cases of arrhythmogenic ventricular cardiomyopathy with different presentations observed over the past 2 years. © 2016, American Society of Nuclear Cardiology.

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Arrhythmogenic cardiomyopathy, Cardiac mri, Sudden death, Ventricular arrhythmias, Adult, Arrhythmogenic right ventricular dysplasia, Death, sudden, cardiac, Diagnosis, differential, Female, Humans, Magnetic resonance imaging, cine, Male, Middle aged, Ventricular dysfunction, left, Ventricular dysfunction, right, Young adult, Gadolinium, Article, Cardiovascular magnetic resonance, Cardioversion, Case report, Contrast enhancement, Electrocardiogram, Emergency ward, Epicardial fat, Heart ejection fraction, Heart left ventricle enddiastolic volume, Heart right ventricle dysplasia, Heart right ventricle enddiastolic volume, Human, Hypertension, Nausea and vomiting, Priority journal, Sudden cardiac death, T wave, T wave inversion, Cine magnetic resonance imaging, Complication, Diagnostic imaging, Differential diagnosis, Heart left ventricle function, Heart right ventricle function, Procedures

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